BENITIONSClinical Trial Intelligence

Long-Term Evaluation of BIIB067 (Tofersen)

Phase 3 Completed NCT03070119

ConditionALS Caused by Superoxide Dismutase 1 Mutation
PhasePhase 3
SponsorBiogen
StatusCompleted
Enrollment139 participants
InterventionsTofersen
Start dateMar 8, 2017
Completion dateAug 12, 2024
Results postedAug 29, 2025

Summary

The primary objective of the study is to evaluate the long-term safety and tolerability of BIIB067 (tofersen) in participants with amyotrophic lateral sclerosis (ALS) and confirmed superoxide dismutase 1 (SOD1) mutation. The secondary objectives are to evaluate the pharmacokinetic (PK), pharmacodynamic (PD), biomarker effects, and efficacy of BIIB067 administered to participants with ALS and a confirmed SOD1 mutation.

Number of Participants With Treatment Emergent Adverse Events (TEAEs) and Treatment Emergent Serious AEs (TESAEs)

From first dose of the study drug in the current study up to end of follow-up period (up to Week 364) · Participants

233AS101: Part C (Prior Placebo)31 Participants
233AS101: Part C (Prior BIIB067 100 mg)63 Participants
233AS101: Part A and B (All Doses)43 Participants
233AS101: Part C (Prior Placebo)16 Participants
233AS101: Part C (Prior BIIB067 100 mg)33 Participants
233AS101: Part A and B (All Doses)22 Participants

Open in BENITIONS View on ClinicalTrials.gov

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